- Diagnostic test and outcome.
| Patient number | Hemoglobin | CSF protein, control <400 mg/L | CT/ MRI brain & spine | Treatment | Outcome |
|---|---|---|---|---|---|
| 1 | 6-12 g/dl | 1326 mg/L | Encephalomalacia, cortical and cerebellar atrophy, cervical cord lesions from brainstem up to C6 | IVIg, corticosteroids, plasma exchange | Died at the age of 14 |
| 2 | 11 g/dl | - | Normal | IVIg | Walking with canes with high steppage gait |
| 3 | 7-11 g/dl | - | Bilateral thalami, basal ganglia, occipital lobes | IVIg, corticosteroids | Died at the age of 10 |
| 4 | 11-13 g/dl | 685 mg/L | Bilateral thalami, internal capsule, corpus callosum lesions | IVIg, corticosteroids | Standing but not walking, aphasia, intellectual impairment |
| 5 | 8-11 g/dl | - | Normal | IVIg | Flaccid paralysis of lower limbs, just sitting |
| 6 | 7-11 g/dl | 872 mg/L | Extensive demyelination supra and infratentorial structures including brainstem | IVIg, corticosteroids, eculizumab | Persistent vegetative state |
| 7 | 7.5-10 g/dl | - | Right middles artery stroke, left hemispheric atrophy | IVIg | Persistent vegetative state on ventilator support |
| 8 | 7.5-9.9 g/dl | 914 mg/L | Normal | IVIg, plasma exchange | Flaccid lower limbs |